International Journal of Prosthodontics and Restorative Dentistry

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VOLUME 12 , ISSUE 2 ( April-June, 2022 ) > List of Articles


Gunther's Disease: Esthetic Management of Erythrodontia with 1-year Follow-up

Pranjal Sharma, Shanthala B Mallikarjun, Sowndarya Gunasekaran

Keywords : Congenital erythropoietic porphyria, Erythrodontia, Esthetic, Gunther disease, Maxillary anterior teeth, One-step dentin bonding system

Citation Information : Sharma P, Mallikarjun SB, Gunasekaran S. Gunther's Disease: Esthetic Management of Erythrodontia with 1-year Follow-up. Int J Prosthodont Restor Dent 2022; 12 (2):94-96.

DOI: 10.5005/jp-journals-10019-1372

License: CC BY-NC 4.0

Published Online: 25-01-2023

Copyright Statement:  Copyright © 2022; The Author(s).


Intrinsic tooth stains are more permanent in nature than extrinsic stains and can be divided into two types systemic and local. Erythrodontia is reddish-brown or reddish-black discoloration of teeth caused due to congenital erythropoietic porphyria (CEP) or Gunther disease. It is the rarest type of porphyria and is usually perceived in infancy. An 8-year-old girl with erythrodontia was referred to a private clinic in the United Arab Emirates with a chief complaint of discolored primary teeth with a medical history of CEP and severe right sensorineural hearing loss. A complete esthetic rehabilitation was done.

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