International Journal of Prosthodontics and Restorative Dentistry

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VOLUME 1 , ISSUE 1 ( April-June, 2011 ) > List of Articles

CASE REPORT

Prosthodontic Management of Brothers affected from Anhydrotic Ectodermal Dysplasia

Rajiv Kumar Gupta, Thallam Veer Padmanabhan, Bijoy Thomas

Keywords : testing,purpose,Dentistry,Medicine,Nursing

Citation Information : Gupta RK, Padmanabhan TV, Thomas B. Prosthodontic Management of Brothers affected from Anhydrotic Ectodermal Dysplasia. Int J Prosthodont Restor Dent 2011; 1 (1):41-45.

DOI: 10.5005/jp-journals-10019-1007

Published Online: 01-06-2011

Copyright Statement:  Copyright © 2011; The Author(s).


Abstract

Anhydrotic ectodermal dysplasia is a rare congenital disease that can affect several ectodermal structures, such as hair, teeth, skin, nails, sweat and sebaceous glands. It is commonly a difficult condition to manage with prosthodontics because of the typical oral deficiencies and also patients are quite young when they are evaluated for treatment. This clinical report describes the management of two brothers affected by ectodermal dysplasia, prosthodontically. It is important that these patients should get dental treatment at an early stage for physiologic and psychosocial reasons. Dental treatment can vary depending upon the severity of the disease. This case report describes the use of removable partial dentures to replace congenitally missing teeth, and composite resin material to restore the conical maxillary central incisors to achieve a favorable esthetic result. This approach rehabilitates patients without sacrificing healthy dental tissues.


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